The association of multiple congenital dislocations of major joints and characteristic facial abnormalities were first recognized as syndrome by Larsen and co-workers in 1950. A one year old boy presented in this report had multiple congenital joint dislocations, flattened face and short neck which are characteristic of patients with Larsen syndrome. The patient was scheduled for lip and palatal defects under general anaesthesia. Physical examination revealed a Mallampati II airway with intact palate. We used sevoflurane 1-8% and alfentanyl 10μg/kg for anaesthesia induction and 50%N20, O2 and sevoflurane 1-3%, for maintenance. Both induction and maintenance were uneventful. Recovery from anaesthesia was also uneventful.
Keywords: Larsen syndrome, general anaesthesia